Term
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Definition
the ubiquitin proteosome requires what for activation? |
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Definition
what provides the correct pH for gastric enzymes to be active |
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Definition
pancreatic enzymes are released as zymogens. what hormone is responsible for this release |
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Term
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Definition
at the C-terminal this lyses Alanine, Leucine, Isoleucine, Valine |
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Term
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Definition
at the C-terminal this lyses Arginine or Lysine |
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Term
Alanine, Glycine, and Serine |
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Definition
Elastase, which is activated by trypsin, lyses what three AA on the C-side? |
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Term
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Definition
Amino acids require pyridoxal phophate which is derived from? |
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Term
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Definition
Alanine and alpha-ketoglutarate are the reactants and pyruvate and glutamate are the products of this enzyme |
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Term
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Definition
OAA and Glutamate are the reactants and Asparate and alpha ketoglutarae are the products of this enzyme |
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Term
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Definition
Leucine, Lycine, and Tryptophan are the major? |
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Term
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Definition
AR disorder where cystine cant be reabsorbed and leadds to stones of cystine in the urinary tract |
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Term
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Definition
all of the amino acids except these two participate in transamination |
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Term
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Definition
NAD+ and NADP can be used as coenzymes for this enzyme |
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Term
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Definition
what is the allosteric inhibitor of glutamate dehydrogenase? |
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Term
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Definition
what is the allosteric activator of glutamate dehydrogenase? |
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Term
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Definition
what is the precursor for ammonium and asparate nitrogen? |
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Term
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Definition
what allosterically activates carbomyl synthestase I? |
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Term
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Definition
what is the activator of NAG |
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Term
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Definition
how many molecules of ATP are consumed in the formation of UREA |
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Term
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Definition
reduces the number of intestinal bacteria responsible for NH3 production |
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Term
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Definition
how many high energy phosphates are consumed in the synthesis of each mole of urea? |
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Term
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Definition
carbamoyl phosphate synthestase I deficiency is treated with? |
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Term
carbomyl phophate synthetase I |
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Definition
a deficiency in this enzyme, leads to the inability for nitrogenous waste to be metabolized in the urea cycle |
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Term
Orthinine Transcarbomylase |
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Definition
a deficiency in this enzyme leads to a inability for nitrogenous waste to be metabolized and is associated with X-linked inheritance |
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Term
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Definition
a deficiency in this enzyme leads to a elevated serum citrulline count associated with hypotonia, ataxia, and behavioral changes |
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Term
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Definition
a deficiency in this enzyme leads to hyperammonemia and has huge effects on the CNS |
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Term
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Definition
if there is a deficiency in this enzyme there will be no hyperammonemia and there will be restoration of the pathway |
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